Primary lymphoedema at an unusual location triggered by nephrotic syndrome.

INTRODUCTION Lymphoedema results from impaired lymphatic transport leading to the pathologic accumulation of protein-rich lymphatic fluid in the interstitial space, most commonly in the extremities. Primary lymphoedema, a developmental abnormality of the lymphatic system, may become evident later in life when a triggering event exceeds the capacity of normal lymphatic flow. CLINICAL PICTURE We present a 3-year-old nephrotic syndrome patient with an unusual localisation for primary lymphoedema. TREATMENT AND OUTCOME The patient was treated with conservative approach and she was cured. CONCLUSION In this particular case, lymphoedema developed at an unusual localisation, which has not been recorded before.